FOP patients | ≤18y | >18y | Total | ||
---|---|---|---|---|---|
survivors (group A) | non-survivors (group B) | survivors (group C) | non-survivors (group D) | ||
Cases | 40(88.9%) | 5(11.1%) | 16(80%) | 4(20%) | 65 |
Gender ratio (M/F) | 21/19 | 1/4 | 6/10 | 2/2 | 30/35 |
Age at diagnose (years) | 9.6 ± 5.0 | 11.6 ± 6.3 | 24.4 ± 7.1 **△△ | 25.5 ± 2.4 **△△ | 14.4 ± 8.8 |
Age of onset | 3.6 ± 2.9 | 2.3 ± 2.3 | 4.6 ± 4.4 | 3.4 ± 2.2 | 4.2 ± 3.9 |
Age at death (years) | – | 17.4 ± 7.2 | – | 29.5 ± 2.9△△ | 22.8 ± 8.9 |
OC (ng/mL) | 87.7 ± 32.7 | 48.7 ± 15.5** | 34.7 ± 19.8** | 26.8 ± 16.1** | 67.9 ± 37.8 |
Ca (mmol/L) | 2.32 ± 0.2 | 2.34 ± 0.07 | 2.32 ± 0.08 | 2.24 ± 0.05 | 2.32 ± 0.15 |
P (mmol/L) | 1.58 ± 0.25 | 1.42 ± 0.15 | 1.23 ± 0.3** | 1.02 ± 0.21**△ | 1.45 ± 0.31 |
PTH (pg/mL) | 63.3 ± 487.4 | 53.2 ± 25.9 | 81.5 ± 37.7 | 71.9 ± 14.3 | 67.5 ± 42.8 |
ALP (IU/L) | 244.0 ± 121.1 | 128.2 ± 85.0* | 121.9 ± 78.6** | 82.2 ± 24.9* | 192.3 ± 121.9 |
ESR (mm/hr) | 7.9 ± 5.2 | 9.4 ± 8.7 | 10.2 ± 9.2 | 9.25 ± 5.6 | 8.6 ± 7.8 |
ALT (U/L) | 14.9 ± 7.2 | 10.6 ± 3.4 | 15.0 ± 10.6 | 16.7 ± 13.2 | 14.6 ± 8.0 |
AST (U/L) | 24.6 ± 9.7 | 23.1 ± 6.0 | 25.3 ± 10.9 | 19.57 ± 12.7 | 24.3 ± 13.3 |
Cr (umol/L) | 38.0 ± 14.3 | 31.0 ± 5.2 | 46.8 ± 14.0 | 43.7 ± 11.3 | 39.4 ± 14.0 |
BUN (mmol/L) | 2.0–5.8 | 1.7–7.2 | 2.9–6.3 | 2.2–5.3 | 1.7–7.2 |